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| Open AccessThe changing epidemiology of pulmonary infection in children and adolescents with cystic fibrosis: an 18-year experience
- Jagdev Singh
- , Sharon Hunt
- & Hiran Selvadurai
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| Open AccessDual species sphingosine-1-phosphate lyase inhibitors to combine antifungal and anti-inflammatory activities in cystic fibrosis: a feasibility study
- Barbara Cellini
- , Gioena Pampalone
- & Claudio Costantini
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| Open AccessExploring intrinsic variability between cultured nasal and bronchial epithelia in cystic fibrosis
- Lisa W. Rodenburg
- , Mieke Metzemaekers
- & Gimano D. Amatngalim
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| Open AccessCystic fibrosis-related mortality in the United States from 1999 to 2020: an observational analysis of time trends and disparities
- Harpreet Singh
- , Chinmay Jani
- & Justin D. Salciccioli
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| Open AccessHigher levels of Pseudomonas aeruginosa LasB elastase expression are associated with early-stage infection in cystic fibrosis patients
- Agustina Llanos
- , Pauline Achard
- & Martin Everett
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| Open AccessImpact of gas humidification and nebulizer position under invasive ventilation: preclinical comparative study of regional aerosol deposition
- Yoann Montigaud
- , Quentin Georges
- & Sophie Périnel-Ragey
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| Open AccessPredicting glycemic control status and high blood glucose levels through voice characteristic analysis in patients with cystic fibrosis-related diabetes (CFRD)
- Pichatorn Suppakitjanusant
- , Nittaya Kasemkosin
- & Vin Tangpricha
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| Open AccessTherapeutic beta-lactam dosages and broad-spectrum antibiotics are associated with reductions in microbial richness and diversity in persons with cystic fibrosis
- Andrea Hahn
- , Aszia Burrell
- & Edith T. Zemanick
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| Open AccessLipidomic alterations in human saliva from cystic fibrosis patients
- Marianna Caterino
- , Roberta Fedele
- & Giuseppe Castaldo
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| Open AccessSurvival of people with cystic fibrosis in Australia
- Rasa Ruseckaite
- , Farhad Salimi
- & Susannah Ahern
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| Open AccessGenomic epidemiology of Mycobacterium abscessus in a Canadian cystic fibrosis centre
- Nicholas Waglechner
- , Elizabeth Tullis
- & Robyn S. Lee
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| Open AccessClinical characteristics, radiological features, and disease severity of bronchiectasis according to the spirometric pattern
- Sun-Hyung Kim
- , Bumhee Yang
- & Kang Hyeon Choe
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| Open AccessA pilot study of disease related education and psychotherapeutic support for unresolved grief in parents of children with CF
- André Schultz
- , Andrea Barrett
- & Florian Zepf
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| Open AccessA medium composition containing normal resting glucose that supports differentiation of primary human airway cells
- Rachel Morgan
- , Candela Manfredi
- & Samuel A. Molina
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| Open AccessCommon cardiac medications potently inhibit ACE2 binding to the SARS-CoV-2 Spike, and block virus penetration and infectivity in human lung cells
- Hung Caohuy
- , Ofer Eidelman
- & Harvey B. Pollard
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| Open AccessImmunometabolic factors in adolescent chronic disease are associated with Th1 skewing of invariant Natural Killer T cells
- Francesca A. Ververs
- , Suzanne E. Engelen
- & Henk S. Schipper
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| Open AccessSerum inflammatory profiles in cystic fibrosis mice with and without Bordetella pseudohinzii infection
- Paul M. Litman
- , Alexander Day
- & Rebecca J. Darrah
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| Open AccessValidation of nasospheroids to assay CFTR functionality and modulator responses in cystic fibrosis
- Maite Calucho
- , Silvia Gartner
- & Eduardo F. Tizzano
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| Open AccessAutophagy of mucin granules contributes to resolution of airway mucous metaplasia
- J. M. Sweeter
- , K. Kudrna
- & J. D. Dickinson
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| Open AccessVitamin D intoxication in patients with cystic fibrosis: report of a single-center cohort
- Thomas Planté-Bordeneuve
- , Silvia Berardis
- & Sophie Gohy
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| Open AccessAn observational study of anaerobic bacteria in cystic fibrosis lung using culture dependant and independent approaches
- Claudie Lamoureux
- , Charles-Antoine Guilloux
- & Geneviève Héry-Arnaud
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| Open AccessEffects of vitamin D deficiency on the improvement of metabolic disorders in obese mice after vertical sleeve gastrectomy
- Jie Zhang
- , Min Feng
- & Wenxian Guan
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| Open AccessA pilot study of cystic fibrosis exacerbation response phenotypes reveals contrasting serum and sputum iron trends
- Alex H. Gifford
- , Deepika Polineni
- & Jonathan B. Zuckerman
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| Open AccessModulation of cAMP metabolism for CFTR potentiation in human airway epithelial cells
- Jenny P. Nguyen
- , Matthew Bianca
- & Jeremy A. Hirota
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| Open Access(R)-Roscovitine and CFTR modulators enhance killing of multi-drug resistant Burkholderia cenocepacia by cystic fibrosis macrophages
- Chandra L. Shrestha
- , Shuzhong Zhang
- & Benjamin T. Kopp
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| Open AccessRisk factors for respiratory Aspergillus fumigatus in German Cystic Fibrosis patients and impact on lung function
- Uta Düesberg
- , Julia Wosniok
- & Carsten Schwarz
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| Open AccessENaC regulation by phospholipids and DGK explained through mathematical modeling
- Daniel V. Olivença
- , Eberhard O. Voit
- & Francisco R. Pinto
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| Open AccessAltered iron metabolism in cystic fibrosis macrophages: the impact of CFTR modulators and implications for Pseudomonas aeruginosa survival
- H. F. Hazlett
- , T. H. Hampton
- & A. Ashare
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| Open AccessThe changing demography of the cystic fibrosis population: forecasting future numbers of adults in the UK
- Ruth H. Keogh
- , Kamaryn Tanner
- & Diana Bilton
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| Open AccessEvaluation of a five-year predicted survival model for cystic fibrosis in later time periods
- Theodore G. Liou
- , Christiana Kartsonaki
- & Frederick R. Adler
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| Open AccessA randomised controlled trial of rosuvastatin for the prevention of aminoglycoside-induced kidney toxicity in children with cystic fibrosis
- Stephen J. McWilliam
- , Anna Rosala-Hallas
- & Munir Pirmohamed
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| Open AccessPlasma microRNA levels in male and female children with cystic fibrosis
- C. Mooney
- , P. J. McKiernan
- & C. M. Greene
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| Open AccessPulmonDB: a curated lung disease gene expression database
- Ana B. Villaseñor-Altamirano
- , Marco Moretto
- & Alejandra Medina-Rivera
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| Open AccessGut Microbiota in Children With Cystic Fibrosis: A Taxonomic and Functional Dysbiosis
- Michael J. Coffey
- , Shaun Nielsen
- & Chee Y. Ooi
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| Open AccessShort-term consequences of F508del-CFTR thermal instability on CFTR-dependent transepithelial currents in human airway epithelial cells
- Lionel Froux
- , Christelle Coraux
- & Frédéric Becq
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| Open AccessG-CSF and GM-CSF Modify Neutrophil Functions at Concentrations found in Cystic Fibrosis
- Stefano Castellani
- , Susanna D’Oria
- & Massimo Conese
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| Open AccessA BAC Transgene Expressing Human CFTR under Control of Its Regulatory Elements Rescues Cftr Knockout Mice
- Lara R. Gawenis
- , Craig A. Hodges
- & Lane L. Clarke
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| Open AccessHDAC6 depletion improves cystic fibrosis mouse airway responses to bacterial challenge
- Julie Rosenjack
- , Craig A. Hodges
- & Thomas J. Kelley
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| Open AccessA Systematic Review of the Clinical Efficacy and Safety of CFTR Modulators in Cystic Fibrosis
- Al-Rahim R. Habib
- , Majid Kajbafzadeh
- & Bradley S. Quon
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| Open AccessOptimization of the adipose-derived mesenchymal stem cell delivery time for radiation-induced lung fibrosis treatment in rats
- Yang Zhang
- , Xinping Jiang
- & Liqun Ren
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| Open AccessLongitudinal development of the airway microbiota in infants with cystic fibrosis
- Bushra Ahmed
- , Michael J. Cox
- & Andrew Bush
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| Open AccessChanges in microbiome diversity following beta-lactam antibiotic treatment are associated with therapeutic versus subtherapeutic antibiotic exposure in cystic fibrosis
- Andrea Hahn
- , Hani Fanous
- & Keith A. Crandall
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| Open AccessNebulized hypertonic saline triggers nervous system-mediated active liquid secretion in cystic fibrosis swine trachea
- Xiaojie Luan
- , Julian S. Tam
- & Juan P. Ianowski
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| Open AccessImpact of CFTR modulation with Ivacaftor on Gut Microbiota and Intestinal Inflammation
- Chee Y. Ooi
- , Saad A. Syed
- & Tanja Gonska
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| Open AccessInhibition of Wnt/β-catenin signaling suppresses myofibroblast differentiation of lung resident mesenchymal stem cells and pulmonary fibrosis
- Honghui Cao
- , Cong Wang
- & Xiaodong Han
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| Open AccessUrinary Biomarkers of Aminoglycoside-Induced Nephrotoxicity in Cystic Fibrosis: Kidney Injury Molecule-1 and Neutrophil Gelatinase-Associated Lipocalin
- Stephen J. McWilliam
- , Daniel J. Antoine
- & Munir Pirmohamed
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| Open AccessA Mathematical Model of the Phosphoinositide Pathway
- Daniel V. Olivença
- , Inna Uliyakina
- & Francisco R. Pinto
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| Open AccessSilica inhalation altered telomere length and gene expression of telomere regulatory proteins in lung tissue of rats
- Mohammad Shoeb
- , Pius Joseph
- & James M. Antonini
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| Open AccessKlotho Inhibits Interleukin-8 Secretion from Cystic Fibrosis Airway Epithelia
- Stefanie Krick
- , Nathalie Baumlin
- & Matthias Salathe